???? ????? ??????? ????? ?? ??? ??????? ???????? ?? ???? ????? ???????, ?? ???? ????? ????? ?????? ?????? ?????? ???? ???? ???? ?????? ???? ?????, ?? ???? ??? ???? ?????? ?????, ?? ?? ?? ????? ?? ????? ????.

?????? ?????? ??????, ?????? E ??? ?????? ?? ??? ????? ???????? ?????? ?????? ???????? ????????? ?????????? ??????? ???. ???? ?????? ???? ?????, ??? ?? ?? ???? ????? ???? ????? ?? ????? ?????, ????? ????????, ????? ?????? ???? ???'.

Cysteamine (Cysteamine,CS), ????? ?? ??? β-merhydrylethylamine, ???? ?????? ????, ????? ???? 99 ~ 100 ℃, ??? ???, ???? ???? ????????, ????? ???????. ?????? ???? ???? ?????? sulfhydryl ?????? ??????, ?? ?? ????? ???????? ?????????. ??? ???? ???? ???????? ????? ???? ??? ?? ?????? ??????????? ??????.

L ??????? ??????????? ??? ???? ???? ????? ????? ???? ????. ???? ?????? ???? ???? ??????, ????? ????? ????? ?????? ???? ????, ?-??????? ???? ?????? ???? ?? ?????? ???? ???? ????? ??? ????, ???????, ?????? ?? ???? ????? ??????? ?????.

?????????? ??? ?? ???? ?????? ???????? ?????? ????. ???? ????, ??? ??? ?????.

?????? ??? ?? ????, ???? ???? ???????? ????? ????? ????. ??? ?? ????? ?????? ?? ?????? ?????? ??????? ???? ???? ??? ????.

????? ???????? ?? ??? ?? ???? ?? ???? ?????? ?? ??? ?????? ?????? ?? ??? ????, ?? ???? ?????? ?? ??? ???? ?? ?????? ??????????? ????? ???? ??????.

????? ??? ?? ?????? ?????? ?? ?????, ????, ???????? ?????? ????? ?????, ?? ?? ?????? ??? ??????? ????, ?? ???? ?-70, ????? ???????? ?????? ????? ?????? ?????????, ?????? ?"???? ????? ??????", ??? ???? ???? ???? ????? ????.

?????? ??? ?? ????, ?????? ???????? ??? ?? ?????? ????????? ??? ?? ??????? ???????? ???? ????-1, 2-????????. ????? ????????? ??? ???? ?????? ?????, ????? ?? ???? ??? ????????? ????????, ??? ?????? ???????.